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  1. 1.   ALS/FTD-Linked Mutation in FUS Suppresses Infra-axonal Protein Synthesis and Drives Disease Without Nuclear Loss-of-Function of FUS
  2. Lopez-Erauskin, Jone; Tadokoro, Takahiro; Baughn, Michael W.; Myers, Brian; McAlonis-Downes, Melissa; Chillon-Marinas, Carlos; Asiaban, Joshua N.; Artates, Jonathan; Bui, Anh T.; Vetto, Anne P.; Lee, Sandra K.; Le, Ai Vy; Sun, Ying; Jambeau, Melanie; Boubaker, Jihane; Swing, Debbie; Qiu, Jinsong; Hicks, Geoffrey G.; Ouyang, Zhengyu; Fu, Xiang-Dong; Tessarollo, Lino; Ling, Shuo-Chien; Parone, Philippe A.; Shaw, Christopher E.; Marsala, Martin; lagier-Tourenne, ClotilDe; Cleveland, Don W.; Da Cruz, Sandrine
  3. Neuron. 2018, NOV 21; 100(4): 816-+.
  1. 2.   Behavioral and Molecular Exploration of the AR-CMT2A Mouse Model Lmna (R298C/R298C)
  2. Poitelon, Y.; Kozlov, S.; Devaux, J.; Vallat, J. M.; Jamon, M.; Roubertoux, P.; Rabarimeriarijaona, S.; Baudot, C.; Hamadouche, T.; Stewart, C. L.; Levy, N.; Delague, V.
  3. Neuromolecular Medicine. 2012, Mar; 14(1): 40-52.
  1. 3.   Islet1-mediated activation of the beta-catenin pathway is necessary for hindlimb initiation in mice
  2. Kawakami, Y.; Marti, M.; Kawakami, H.; Itou, J.; Quach, T.; Johnson, A.; Sahara, S.; O'Leary, D. D. M.; Nakagawa, Y.; Lewandoski, M.; Pfaff, S.; Evans, S. M.; Belmonte, J. C. I.
  3. Development. 2011, Oct; 138(20): 4465-4473.
  1. 4.   Embryonic stem cell-derived motoneurons provide a highly sensitive cell culture model for botulinum neurotoxin studies, with implications for high-throughput drug discovery
  2. Kiris, E.; Nuss, J. E.; Burnett, J. C.; Kota, K. P.; Koh, D. C.; Wanner, L. M.; Torres-Melendez, E.; Gussio, R.; Tessarollo, L.; Bavari, S.
  3. Stem Cell Research. 2011, May; 6(3): 195-205.
  1. 5.   Axonal Mitochondrial Clusters Containing Mutant SOD1 in Transgenic Models of ALS
  2. Sotelo-Silveira, J. R.; Lepanto, P.; Elizondo, V.; Horjales, S.; Palacios, F.; Martinez-Palma, L.; Marin, M.; Beckman, J. S.; Barbeito, L.
  3. Antioxidants & Redox Signaling. 2009 11(7): 1535-1546.
  1. 6.   Onset and progression in inherited ALS determined by motor neurons and microglia
  2. Boillee, S.; Yamanaka, K.; Lobsiger, C. S.; Copeland, N. G.; Jenkins, N. A.; Kassiotis, G.; Kollias, G.; Clevel, D. W.
  3. Science. 2006, JUN 2; 312(5778): 1389-1392.
  1. 7.   Parkinson's disease alpha-synuclein transgenic mice develop neuronal mitochondrial degeneration and cell death
  2. Martin, L. J.; Pan, Y.; Price, A. C.; Sterling, W.; Copeland, N. G.; Jenkins, N. A.; Price, D. L.; Lee, M. K.
  3. Journal of Neuroscience. 2006, JAN 4; 26(1): 41-50.
  1. 8.   Coincident thresholds of mutant protein for paralytic disease and protein aggregation caused by restrictively expressed superoxide dismutase cDNA
  2. Wang, J.; Xu, G. L.; Slunt, H. H.; Gonzales, V.; Coonfield, M.; Fromholt, D.; Copeland, N. G.; Jenkins, N. A.; Borchelt, D. R.
  3. Neurobiology of Disease. 2005, DEC; 20(3): 943-952.
  1. 9.   Inherited motor neuron disease in domestic cats: A model of spinal muscular atrophy
  2. He, Q. C.; Lowrie, C.; Shelton, G. D.; Castellani, R. J.; Menotti-Raymond, M.; Murphy, W.; O'Brien, S. J.; Swanson, W. F.; Fyee, J. C.
  3. Pediatric Research. 2005, MAR; 57(3): 324-330.
  1. 10.   New insights on the evolution of the SMN1 and SMN2 region: simulation and meta-analysis for allele and haplotype frequency calculations
  2. Ogino, S.; Wilson, R. B.; Gold, B.
  3. European Journal of Human Genetics. 2004, DEC; 12(12): 1015-1023.
  1. 11.   Copper-binding-site-null SOD1 causes ALS in transgenic mice: aggregates of non-native SOD1 delineate a common feature
  2. Wang, J.; Slunt, H.; Gonzales, V.; Fromholt, D.; Coonfield, M.; Copeland, N. G.; Jenkins, N. A.; Borchelt, D. R.
  3. Human Molecular Genetics. 2003 12(21): 2753-2764.
  1. 12.   Copper chaperone for superoxide dismutase is essential to activate mammalian Cu/Zn superoxide dismutase
  2. Wong, P. C.; Waggoner, D.; Subramaniam, J. R.; Tessarollo, L.; Bartnikas, T. B.; Culotta, V. C.; Price, D. L.; Rothstein, J.; Gitlin, J. D.
  3. Proceedings of the National Academy of Sciences of the United States of America. 2000 97(6): 2886-2891.
  1. 13.   Axonal Transport of Mutant Superoxide Dismutase 1 and Focal Axonal Abnormalities in the Proximal Axons of Transgenic Mice
  2. Borchelt, D. R.; Wong, P. C.; Becher, M. W.; Pardo, C. A.; Lee, M. K.; Xu, Z. S.; Thinakaran, G.; Jenkins, N. A.; Copeland, N. G.; Sisodia, S. S.; Clevel, D. W.; Price, D. L.; Hoffman, P. N.
  3. Neurobiology of Disease. 1998 5(1): 27-35.
  1. 14.   Using Ec and Es Cell Culture to Study Early Development - Recent Observations On Indian Hedgehog and Bmps
  2. Grabel, L.; Becker, S.; Lock, L.; Maye, P.; Z, ers
  3. International Journal of Developmental Biology. 1998 42(7 Special Issue SI): 917-925.
  1. 15.   Thiol oxidation and loss of mitochondrial complex I precede excitatory amino acid-mediated neurodegeneration
  2. Sriram, K.; Shankar, S. K.; Boyd, M. R.; Ravindranath, V.
  3. Journal of Neuroscience. 1998 18(24): 10287-10296.
  1. 16.   Paired-Related Murine Homeobox Gene Expressed in the Developing Sclerotome, Kidney, and Nervous System
  2. Mansouri, A.; Yokota, Y.; Wehr, R.; Copeland, N. G.; Jenkins, N. A.; Gruss, P.
  3. Developmental Dynamics. 1997 210(1): 53-65.
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