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Coronary Abnormalities in Hyper-IgE Recurrent Infection Syndrome: Depiction at Coronary MDCT Angiography

  1. Author:
    Gharib, A. M.
    Pettigrew, R. I.
    Elagha, A.
    Hsu, A.
    Welch, P.
    Holland, S. M.
    Freeman, A. F.

  2. Author Address

    Gharib, Ahmed M.; Elagha, Abdalla] NIDDKD, Dept Radiol, NIH, Clin Res Ctr, Bethesda, MD 20892 USA. [Pettigrew, Roderic I.] Natl Inst Biomed Imaging & Bioengn, NIH, Bethesda, MD USA. [Hsu, Amy, Holland, Steven M.; Freeman, Alexandra F.] NIAID, NIH, Bethesda, MD 20892 USA. [Welch, Pam] NCI, SAIC Frederick, Frederick, MD 21701 USA.
    1. Year: 2009
  2. Journal: American Journal of Roentgenology
    1. 193
    2. 6
    3. Pages: W478-W481
  4. Type of Article: Article
  5. ISSN: 0361-803X
  1. Abstract:

    OBJECTIVE. Hyper-IgE recurrent infection syndrome (HIES or Job's syndrome) is a rare disorder affecting the immune system and connective tissues. The purpose of this study is to describe the coronary abnormalities in genetically confirmed HIES patients as depicted by coronary MDCT angiography (MDCTA). CONCLUSION. Coronary MDCTA has provided an opportunity for noninvasive evaluation of the coronary arteries in patients with HIES. These coronary abnormalities vary from tortuosity to ectatic dilation and focal aneurysms of the coronary arteries. Such an evaluation has potential value in identifying new aspects of this disease and thereby providing better understanding of the pathophysiology of the disorder.

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External Sources

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  2. DOI: 10.2214/ajr.09.2623
  3. PMID: 19933621

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